Steroid-Boikarabello ba Encephalopathy e kopantsoeng le / Autoimmune Thyroiditis
Lefu le tsejoang e le " Hashimoto's Encephalopathy " le ile la hlalosoa ka lekhetlo la pele ka 1966. Ka mor'a nako eo, lingaka li ile tsa qala ho bokella litlaleho tsa litaba, 'me "Hashimoto's Encephalopathy" e ile ea e-ba lebitso le amohelehang bakeng sa boemo ba ho fokotsa lefu le amanang le Hashimoto's thyroiditis.
Hobane bakuli ba bangata ba nang le Hashimoto's Encephalopathy ba ntlafatsoa ke li-steroids kapa phekolo ea immunosuppressant, litsebi tse ling hona joale li bua ka boemo bona e le "lefu la steroid-le amohelehang le amang lefu le amanang le autoimmune thyroiditis" (SREAT).
Maemong a mang, boemo bona bo ka boela ba bitsoa "nonvasculitic autoimmune meningoencephalitis" (NAIM), e ke keng ea kenyelletsa mathata a qoqotho ea qoqotho feela empa e boetse e akarelletsa mathata a mang a boipheliso a kang Sjögren syndrome le systemic lupus erythematosus-e amanang le meningoencephalitis. Se tloaelehileng har'a maemo ana kaofela ke hore ba arabela kalafo ea steroid.
Poleloana "ho se fele pelo" e bolela lefu la boko le etsang hore boko bo sebetse kapa bo sebetse. Karolo e ka sehloohong ea ho fokola ha pelo ho fetoloa kelellong. Le hoja matšoao a itšetlehile ka mofuta oa ho fokotsa pelo le hore na o tebile hakae, matšoao a tloaelehileng a kenyeletsa:
- ho lahleheloa ke hlooho
- ho thata ho tsepamisa maikutlo
- tahlehelo ea bokhoni ba ho tseba tsebo le mosebetsi
- botho bo fetoha
- lethargy le mokhathala
- ho lahleheloa ke kelello
- myoclonus (ho ikoetlisa ka tsela e ikhethang)
- nystagmus (leihlo le potlakileng leihlo la mahlo)
- ho thothomela
- ho fokola ha mesifa
- 'dementia'
- ho tsieleha, ho tepella
- ho thata ho e metsa
- ho thata ho bua
Matšoao a mang a mang a ka bonoang a kenyeletsa:
- pherekano, ho sithabela
- psychosis
- hlooho ea hlooho
- hemiparesis e nepahetseng ka lehlakoreng le letona - ka lehlakoreng le letona le feletsoe ke ho shoele litho
- mathata a motlakase a tsamaiso ea motlakase - mathata a tsamaisanang le matsoho, matsoho, menoana
Hobane Hashimoto's Encephalopathy / SREAT ha e utloisisoe hampe, thuputsong e tlalehiloeng ka February 2006, Archives of Neurology , litsebi li ile tsa hlahisa likarolo tse sa tšoaneng tsa kliniki, laboratori le litsebi tsa radiologic tsa boemo bona.
Sepheo sa bona ke ho thusa ho ntlafatsa bokhoni ba lingaka ba ho hlokomela le ho hlahloba boemo bona.
Phuputso e ile ea sheba bakuli ba 20 (basali ba 14, banna ba tšeletseng) ba ileng ba fumanoa ba le pakeng tsa 1995 le 2003. Mehla ea bona e bohareng ha ho kula e ne e le lilemo tse 56, ka lilemo tse 27 ho isa ho tse 84 (lilemo tse 27-84).
Mokhoa o tloaelehileng oa ho hlokomela likliniki / matšoao a ne a le:
- Moferefere - 80%
- Palo ea Asia - 80% (bothata ba Aphasia ka puo, ho ama bokhoni ba ho bua, ho bala kapa ho ngola)
- Myoclonus - 65% (ka tšohanyetso, ho itšunya-tšunya ka ho itšehla thajana ea mesifa kapa sehlopha sa mesifa)
- Fumana ataxia - 65% (ho sa tsamaee hantle kapa ho tsamaea ka thata, ho thatafalloa ho tsamaea)
- Lihlahisoa - 60%
- Ho se robale hantle - 55%
Tlhahlobo e mpe ea lithethefatsi ke Standard
Ntho e amehang ka ho khetheha ke hore litsebi li fumane hore BATHO BA MANGATA bohle ba ne ba se ba sa tsejoe. Ka mohlala:
- Encephalitis e nang le viral - 25%,
- Bothata ba 'dementia' e ts'oaetsoang - 20%
- Lefu la Creutzfeldt-Jakob - 15% (lefu la Creutzfeldt-Jakob ke lefu le sa tloaelehang, le fokolang, le fokolang kelellong ea ka linako tse ling, ka linako tse ling le bitsoang "Mad Cow Mafu" bathong)
Litlhapi le Tlhahlobo e sa Lebelloang Hashimoto's Encephalopathy / SREAT
Lintho tse sa tloaelehang tsa teko li ile tsa hlokomeloa, ho akarelletsa:
- Ho eketseha ha sebete sa enzyme - 55%
- Matšoao a li-hormone tsa qoqotho (TSH) a eketsehileng - 55%
- Tekanyo e eketsehileng ea seretse ea erythrocyte ("sed sed") - 25%
- Moriana o sa tloaelehang o nang le metsi a fanang ka maikutlo a ho ruruha - 25%
- Tšoantšiso ea mahlaseli a mahlaseli a mahlahahlaha a maholo a lumellanang le ho fokola ha maikutlo - 26%
Liphello
Bafuputsi ba fihletse qeto ea hore ho na le lintho tse fapa-fapaneng tse ka fumanoang le Hashimoto's Encephalopathy / SREAT, mme mokhoa ona o sa tloaelehang oa ho lemoha maikutlo o tloaelehile.
Bafuputsi ba khothaletsa hore Hashimoto's Encephalopathy / SREAT e lokela ho nkoa esita le haeba TSH le "sed rate" li tloaelehile, cerebrospinal fluid ha e bontše bopaki ba ho ruruha 'me MRI e tloaelehile.
Bakeng sa boitsebiso bo eketsehileng
Hashimoto's Encephalopathy Information Page
> Mohloli
> Castillo, Pablo MD; le. al. "Steroid-e Nang le Boikutlo bo Nang le Bokooa bo Nang le Bokooa bo Tšoanang le Autoimmune Thyroiditis." Arch Neurol . 2006; 63: 197-202. (Khaolo ea 63 No. 2, February 2006)
> Setsi sa Sechaba sa Mathata a Ts'oaetso le Lefu