Co-Occurrence ea mafu a ikhethang
Multiplemmune syndrome, ka tlhaloso, ke ketsahalo e kopanetsoeng ea bonyane maloetse a mararo a motho a le mong ho motho a le mong. Hoo e ka bang karolo ea 25 lekholong ea ba nang le lefu lena ka boithaopo ba na le tšekamelo kapa monyetla oa ho hlaolela mafu a mang a se nang boipheliso. Batho ba nang le methapo e mengata ea autoimmune ba atisa ho ba le boemo bo le bong ba dermatological (letlalo), seo hangata se leng vitiligo kapa alopecia areata .
Ho ikopanya ha mafu a mahlano a mabeli ho nkoa e le ntho e sa tloaelehang haholo.
Litlhahlobo tsa Multiple Autoimmune Syndrome
Lenane la lihlopha le ile la etsoa bakeng sa batho ba nang le maloetse a mabeli a ikhethileng ka bomong a thehiloeng ho ata ha maemo a mang a hlahang hammoho. Lenaneo la lihlopha, le arohanang likokoana-hloko tse ngata tsa autoimmune ka mefuta e meraro, le molemo bakeng sa ho lemoha boemo bo bocha ha matšoao a qala ho hlaha. E thusa ho fumana hore na boemo ba boraro bo ka 'na ba "kena ka hokae."
- Type 1 Multiple Autoimmune Syndrome - myasthenia gravis , thymoma, polymyositis , giant cell myocarditis
- Mofuta oa 2 Motlakase oa Multiimmune Syndrome - Sjogren's syndrome , lefu la ramatiki , lefu la pele la biliary, scleroderma , lefu la qoqotho le ikhethang
- Mofuta oa 3 o mongata oa autoimmune Syndrome - autoimmune lefu la thyroid, myasthenia gravis le / kapa thymoma, lefu la Sjogren's, lefu la phokolo ea mali, lefu la Addison, mofuta oa lefu la tsoekere la mofuta oa 1, vitiligo, autommune hemolytic anemia, systemic lupus erythematosus , dermatitis herpetiformis
Lebaka la Multiimmune Syndrome
Mokhoa o ka sehloohong o lebisang ho multipleimmune syndrome ha o utloisisoe ka botlalo. Seo se ile sa re, bafuputsi ba belaella hore ho ameha lintho tse bakang tikoloho le liphatsa tsa lefutso. Ho boetse ho tsejoa hore mefuta e meng ea li-autoantibodies e teng maemong a mang le mekhoa e mengata ea litho tsa 'mele e ka ameha.
Hobane maemo a mangata a ho itšehla thajana a ka etsahala ho motho a le mong, kapa ka hare ho lelapa, mekhoa ea immunogenetic e amanang le ho itokisetsa likoloi e ameha.
Litholoana tse hlahang tlhahlobo ea meta e hatisitsoeng ka Nature Medicine (2015) li senoletse hore maloetse a 10 a se nang boithaopo a qalileng ho tloha bongoaneng, ho ne ho e-na le matšoao a liphatsa tsa lefutso tse 22 a arolelanoeng ke maloetse a mabeli kapa a mangata 'me 19 a arolelanoa ke maloetse a mararo a mangata. Matšoao a mangata a liphatsa tsa lefutso a fumanoeng a ne a le litseleng tse amanang le ts'ebetso ea sele, ho ata ha sele, le mekhoa ea ho paka e nang le karolo ea bohlokoa tsamaisong ea ' mele ea ho itšireletsa mafung -le mekhoa ea ho itšireletsa mafung , haholo-holo. Matšoao a 10 a lefu la seoa e ne e le mofuta oa lefu la tsoekere , lefu la li-celiac , lefu lena la bana ba nang le lefuba la masapo , lefu le tloaelehileng la immunodeficiency, mafu a Crohn, lefu la ulcerative, psoriasis , autoimmune thyroiditis le ankylosing spondylitis .
Liphuputso tse ling tsa liphatsa tsa lefutso tsa lefutso li fumanoe liphatsa tsa lefutso tsa makholo a mangata har'a maloetse ao motho a nang le 'ona a amanang le batho ba baholo. Ha ho tsebahatsa liphatsa tsa lefutso ho re thusa ho utloisisa sesosa sa meriana e mengata ea autoimmune, e ka boela ea lebisa litsing tse ling tsa phekolo.
Le hoja lihlopha tse ling tsa liphatsa tsa lefutso le tse hlahisang tikoloho ke mehopolo ea morao-rao, tse ling tse ka hlahisoang ke bafuputsi.
Ho 'nile ha boleloa hore ha lithethefatsi tsa immunomodulatory li hlahisoa ho phekola boloetse bo le bong bo ikhethang, liphetoho tsamaisong ea' mele ea ho itšireletsa mafung li ka 'na tsa e-ba teng tse tsamaisang nts'etsopele ea lefu le leng le le leng la' mele.
Matšoao a mabeli kapa a mangata a ho itšireletsa ho Rheumatology
Ho kopana ha maloetse a mabeli kapa a fetang a mangata ho sa nkoa e le ntho e sa tloaelehang. Hangata ho bonoa ka systemic lupus erythematosus, ramatiki ea ramatiki, scleroderma, lefu la Sjogren, vasculitis le polymyositis.
Liphuputso li bontšitse hore ramatiki ea ramatiki le thyroiditis ea autoimmune ke tse ling tsa maloetse a tloaelehileng a tloaelehileng a fumanehang ho batho bohle.
Ho ea ka Healio Rheumatology, haeba motho e mong a e-na le maemo a mabeli, kotsi ea ho hlahisa e 'ngoe ke 1.5 linako tse ling tse phahameng ho feta ba sa nang le maemo.
Ho thahasellisang ke hore ho na le kamano e fapaneng pakeng tsa ramatiki ea lefuba le multiple sclerosis , e bolelang hore haeba u na le e 'ngoe ea maemo a mabeli, ho na le ts'oaetso e fokotsehang ho hlahisa tse ling. Le hoja ka sebele re ka bitsa taba ena e hlollang, liphatsa tsa lefutso li ka fana ka lebaka la lona.
Ke habohlokoa hore re bolelle hore maloetse a mangata a tloaelehileng a atile haholo ho basali ho feta banna. Phapang ea tekano e phaella ka bothata ba bafuputsi ba lekang ho netefatsa kotsi ea ho ba le boemo bo bobeli ba boipheliso kapa meriana e mengata ea autoimmune syndrome. Na kotsi e joalo ho banna le basali? Ho hongata ho sa ntse ho lokela ho ithutoa.
Lentsoe le Tsoang ho
Bakeng sa batho ba nang le boemo bo le bong bo ikemetseng, ho tlameha hore ho tsoele pele ho falimeha bakeng sa ntshetsopele ea maemo a mang a boipheliso. Hoa tsebahala hore maloetse a mangata a mangata a hlahelang a hlaha ka makhetlo a eketsehileng har'a ba nang le bonyane boemo bo le bong bo ikemetseng. Kamehla bua ka liphetoho tseo u li bonang boemong ba hau le ngaka ea hau. Tlhahlobo ea pele le phekolo ea pele e sebetsa ho uena.
> Mehloli:
> Anaya JM le al. Syndromes ea Multiplemmune Syndromes. Matšoao a ho lemoha ka mafu a ikhethang. Mokokotlo. 2008.
> Cojocaru M, le al. Hangata Autoimmune Syndrome. Maedica (Buchar). April 2010.
> Li YR et al. Ho hlahloba litlhahlobo tsa Shared Genetic Architecture ho na le mafu a leshome a ikhethileng. Nature Medicine 2015.
> Ho tsoela pele ka mathata a mangata a ho itima lijo ka boithaopo. Healio Rheumatology. August 2016.