Lymphangiomatosis le Lymph System

Lymphangiomatosis ke lefu leo ​​ho lona li-tumor tse ngata (lymphangiomas) kapa li-cysts li hōlang tsamaisong ea lymph ea 'mele. Le hoja lihlahala tsena ha li na kankere, li hlasela likarolo tsa 'mele' me li baka bohloko, ho phefumoloha ho thata le matšoao a mang a sa tšoaneng ho itšetlehile ka hore na li hlaha hokae. Lymphangiomas e ka 'na ea hōla masapong, lihlahisoa tse sebetsang, le litho tsa' mele, 'me li ka thibela, ho qobella kapa ho senya likokoana-hloko.

Se bakang lymphangiomatosis ha e e-s'o tsejoe.

Lymphangiomatosis e atisa ho fumanoa ho masea le bana ba banyenyane empa e ka ba teng ka nako leha e le efe. E ama banna le basali ba merabe eohle. Hobane lymphangiomatosis e sa tloaeleha ebile e thata ho e fumana hantle, ha e tsejoe hantle hore na batho ba bangata ba angoa ke eng lefatšeng lohle.

Matšoao

Matšoao a lymphangiomatosis a itšetlehile ka moo lihlahala li ntseng li hōla 'meleng.

Ha nako e ntse e ea, masapo a mang kapa a mang a ka nkeloa sebaka ke lymphangioma, e tsejoang e le lefu la Gorham. Lymphangiomas ha e hōle bokong hobane tsamaiso ea lymph ha e fetelle ho eona.

Tsejoa

Tlhahlobo ea lymphangiomatosis e thehiloe matšoao le boteng ba lymphangiomas tse ngata 'meleng. Tšoantšiso ea CT (computed tomography) le setšoantšo sa motlakase (magnesium resonance imaging) (MRI) se sebelisetsoa ho hlahloba lefu lena. Sampula ea 'mele (biopsy) e nkoa ho thusa ho netefatsa hore lihlahala ke lymphangiomas.

Phekolo

Lymphangiomatosis e lieha ho feta nako. Ha li-tumor li ntse li hōla, li ka baka matšoao a tebileng, a mang a ka 'nang a beha bophelo ba hae kotsing, joalo ka ho baka mokelikeli ho potoloha matšoafong a thibelang ho phefumoloha. Ho tloswa ha li-tumor ho ka khoneha, empa lihlahala tse ling li ka ba thata ho li tlosa ka ho feletseng haeba li phatlalalitse. Meriana e bitsoang Intron A (interferon alfa), chemotherapy, kapa phekolo ea radiation e ka thusa ho phekola lefu lena. Mefuta e meng ea phekolo ea meriana kapa ea ho buuoa e ka thusa ho fokotsa tse ling tsa matšoao kapa mathata a bakoang ke lymphangiomatosis. Ka mohlala, seipone se ka kenngoa ka sefubeng (thoracentesis) ho tlosa metsi a mangata, kapa ho buuoa ho ka etsoa mokokotlong ho felisa methapo ea pinched.

Lisebelisoa:

> "Mabapi le Lymphangiomatosis." Lymphangiomatosis & Khmer's Disease Alliance. 06 Sep 2007. Lymphangiomatosis & Gorham's Disease Alliance.

> Marom, Edith, Cesar Moran, & Reginald Munden. "Generalized Lymphangiomatosis." American Journal of Roentgenology 182 (2004): 1068.

> Rostom, Y. "Phekolo ea thoracic lymphangiomatosis." Litlaleho tsa Maloetse Nakong ea Bongoaneng 83 (2000): 138-139.