Tsoelo-pele ea Patlisiso ea Biogenetic e Fetisetsa Bophelo ba Bophelo
Cystic fibrosis (CF) ke lefu le tsoelang pele le amang bophelo bohle le nako ea bophelo ho ba phelang le lefu lena. Le hoja e le lefu le sa tloaelehang (le amang batho ba ka bang 30 000 feela), le ntse le nkoa e le e 'ngoe ea mathata a liphatsa tsa lefutso a fokolang ka ho fetisisa bophelong.
Le hoja nako ea bophelo ea batho ba nang le CF e ntse e le tlaase ho feta ea baahi ba bangata, ho tseba ho eketsehileng ka lefu lena, hammoho le phekolo e sebetsang haholoanyane , ho qalile ho fetola lintho.
Tšepo ea Bophelo e Fumana Batho ba nang le Cystic Fibrosis
Ka 1938, ha CF e tsejoa e le boloetse, masea a mangata a fumanoeng a e-na le lefu lena a shoa pele a tsoaloa. Lilemong tsa bo-1950, batho ba nang le CF ba ne ba phela nako e teletsana empa ha hoa ka ha e-ba bonolo hore ba fete bongoaneng. Le hoja lintho li ile tsa qala ho ntlafala lilemong tsa bo-1980, ha batho ba se ba le bohareng ba lilemo tse mashome a mabeli, ha hoa ka ha e-ba joalo ho fihlela ho sibolloa ha CFTR ea lefutso ka 1989 hore re ile ra qala ho bona phetoho.
Kajeno, ba hlometseng ka kutloisiso e ntlafetseng ea mekhoa ea liphatsa tsa lefutso tsa CF, re na le mekhoa ea ho laola lefu lena, ho thibela tšoaetso, le ho ntlafatsa tšebetso ea matšoafo ho ba phelang le lefu lena.
Ka lebaka leo, karolelano ea bophelo ea batho ba phelang le CF kajeno ke lilemo tse 37,5. Lefatšeng le tsoetseng pele, palo eo e phahame le ho hakanngoa ho tloha ho lilemo tse 42 ho ea ho tse 50.
Ka tsoelo-pele ea kalafo le theknoloji ea biotechnology, bafuputsi ba bolela esale pele hore masea a hlahileng kajeno a ka khona ho phela hantle ho feta letsatsi la tsoalo la bo 50.
Bophelo bo Ntseng bo Eketseha bo Sireletsa ho Sebelisa Likokoana-hloko
Hoo e ka bang karolo ea 80 lekholong ea batho ba nang le cystic fibrosis ba tla fumana tšoaetso ea Pseudomonas aeruginosa , libaktheria tse tloaelehileng li nka ho ata hohle lefatšeng lohle.
Batho ba nang le CF ba kotsing e khōloanyane ea P. aeruginosa , tšoaetso ea eona e ka lebisang ho phefumoloha ho phefumoloha esita le lefu.
Ha e le hantle, karolo ea 50 lekholong ea batho ba nang le CF ba kenngoeng sepetlele bakeng sa P. aeruginosa ba tla shoa ka lebaka la tšoaetso.
Ka lehlohonolo, ho na le lithethefatsi tse ngata kajeno tse ka tšoarang le ho thibela tšoaetso ea P. aeruginosa . Tsena li kenyelletsa lithibela-mafu tobramycin, levofloxacin, ciprofloxacin, azithromycin, le cephalosporins e atolositsoeng. Hangata khetho ea lithethefatsi e thehiloe litekong tsa ho fumana hore na khatello ea Pseudomonas e ea kae ho khetho e fapaneng ea lithibela-mafu.
Tsamaiso e fapana le mofuta le sebaka sa tšoaetso. Hangata ho tobrled tobramycin kapa levofloxacin e atisa ho fuoa likhoeli ka nako ho thibela kgolo ea baktheria. Ciprofloxacin ea molomo le azithromycin e ka sebelisoa ho thibela tšoaetso kapa ho phekola tšoaetso e teng.
P. aeruginosa e ka boela ea phekoloa ka mofuta oa penicillin o bitsoang ureidopenicillin.
Lintlafatso Tse Ling Ts'ebetsong ea Cystic Fibrosis
Ho phaella mefuteng e meng e sebetsang ea phekolo ea lithibela-mafu, ho ile ha etsoa tsoelo-pele e meng ea phekolo ea mafu a mabeli a matšoafo le a CF. Li akarelletsa:
- pheko ea li-enzyme tse nang le pancreatic ho hlōla mathata a ts'ebetso ea mocheso ka lebaka la ho hlahisa li-mucus kahare
- Pulmozyme (dornase alfa) e hlahisang li-mucus tse thibelang tsela e tsamaeang ka tseleng
- li-bronchodilator (li-inhalants tse bolokang litemana tse bulehileng)
- meriana e khahlanong le ho ruruha
- ho kenyelletsa saline ea hypertonic ho eketsa boholo ba sodium e lahlehileng lifofane
Lintho tsena tsohle li kenya letsoho ho eketsehileng ha litekanyetso tsa pholoho ho batho ba nang le CF.
Lentsoe le Tsoang ho
Cystic fibrosis ke lefu le fapaneng ho feta kamoo e neng e le lilemo tse 20 kapa tse 30 tse fetileng. Kajeno, batho ba nang le CF ba ka phela bophelo bo matla le bo khotsofatsang, ba ea k'holejeng, ba fumana mesebetsi, 'me ba rera lelapa. Ntho e hlileng e ntseng e nka ke mehato e tšeletseng ea ho netefatsa bophelo bo bolelele le bo botle:
- ho utloisisa mekhoa ea hau ea phekolo le ho e nka joalokaha e laetsoe
- ho etsa bonnete ba hore ho ja lijo tse nang le phepo e nepahetseng le lik'hilojule tse fetang 50 lekholong
- ho noa metsi a mangata hore u lule u le metsi hantle
- ho etsa moralo oa ho ikoetlisa o nang le koetliso le koetliso ea cardio
- ho qoba tšoaetso ka ho hlatsoa matsoho, ho fumana liente tsa hau le ho qoba ba bang ba kulang
- ho bona ngaka ea hau khafetsa ho netefatsa hore ts'ebetso ea tlhokomelo e tsitsitseng
Qetellong, cystic fibrosis hase polelo ea lefu eo e kileng ea e-ba eona, 'me, ka tlhokomelo e nepahetseng le kalafo, ha ho na lebaka leo u ke keng ua feta ka litebello tsa boleng le boholo ba bophelo.
> Mohloli:
> O'Sullivan, B. le Freedman, S. "Cystic fibrosis." Lancet . 2009; 373 (9678): 1891-1904.