Klinefelter syndrome 47, XXY

Bothata ba Klinefelter kapa 47, XXY ?:

Klinefelter syndrome ke mokhoa o sa tloaelehang oa liphatsa tsa lefutso moo motho a nang le X chromosome e eketsehileng. Maemo a mang a amanang le Klinefelter ke hypothyroidism, ho hloka matla, kankere ea testicular, le kotsi e eketsehileng ea kankere ea matsoele ea matsoele.

Lintlha tse ling ke life ?::

Chromosomes le lefu la Klinefelter, 47XXY:

Hangata batho ba na le li-chromosome tse peli tsa thobalano seleng ka 'ngoe. Tsehali li na le li-chromosome tse peli tsa X, 'me banna ba na le X le e le' ngoe Y. Batona ba nang le lefu la Klinefelter ba atisa ho ba le kopi e le 'ngoe ea chromosome ea X, bakeng sa li-chromosome tse 47 ka sele; sena se bitsoa (47, XXY.) Banna ba bang ba nang le lefu la Klinefelter ba na le X chromosome e eketsehileng ka lisele tsa bona feela; sena se bitsoa "mosaic 46, XY / 47, XXY." Likopi tse ling tsa X chromosome li kena-kenana le ts'ebetso ea botona le botšehali ea ho kopanela liphate le testicular, kahoo li hlalosa maemo a boletsoeng ka holimo.

Lebaka la lefu la Klinefelter:

Klinefelter syndrome ha e na boemo bo futsitsoeng empa e etsahala ka tšohanyetso. Hangata e bakoa ke phoso e hlahang nakong ea ho arohana ha sele ha ho ntse ho thehoa lehe kapa manonyeletso. Ka mohlala, lehe kapa peo ea semela e ka ba le kopi e eketsehileng ea X chromosome ka lebaka la ho arohana ha sele e fosahetseng.

Haeba e 'ngoe ea lisele tsena e ameha ho emoloa, phello ke ngoana ea nang le chromosome e eketsehileng ea X lisele tsa' mele ka 'ngoe. Ha phoso ea ho arohana ha seleng e hlaha hang-hang khōlong ea bokhachane (ho e-na pele ho manyolo) phello ke mosaic, ho bolelang hore ha ho sele e 'ngoe le e' ngoe 'meleng e amehang.

Tšusumetso ho Monna:

Ho tloha ka 47XX e ka 'na ea se ke ea e-ba teng seleng e' ngoe le e 'ngoe' meleng, boemo bo bong le bo bong bo fapane. Hase matšoao 'ohle a ka hlahang,' me maemong a mangata a sa tsejoe. Mathata a tloaelehileng ka ho fetisisa ke:

Litlhare:

Testosterone e ka fanoa ka therapeutically, ho thusa ntlafatso ea 'mele ha monna e ntse e tsoela pele ka matla. Haeba testosterone e fanoa bakeng sa lefu la Klinefelter, e tlameha ho tsoelapele ka nako e telele bakeng sa bophelo bohle.

Hormonal therapy e ke ke ea ntlafatsa fertility, empa testicular sperm extraction le in vitro fertilization e ka thusa ho fella ka ho ima.

Haeba monna ea hōlileng tsebong a e-na le bothata ba ho tseba ho kopanela liphate kapa ho se sebetse ka thobalano, tlhabollo ea litsebi e ka thusa.

Likamano le Gynecomastia le Kankere ea Bokhachane ea Motho:

Klinefelter syndrome e amahanngoa le kotsi e eketsehileng ea ho ba le kankere ea matsoele ea matsoele. Gynecomastia (maqhubu a tummeng a motona) ke letšoao le le leng la Klinefelter syndrome. Ho ba le meno e meng ea matsoele ho eketsa kotsi ea ho ba le kankere ea matsoele.

Litlhahiso:

Mekhatlo ea Sechaba ea Bophelo. Klinefelter Syndrome ke eng? Ho utloisisa Klinefelter Syndrome. Nako ea ho qetela e tsosolositsoeng: 15 August 2006. Klinefelter Syndrome ke eng?

Mokhatlo oa Amerika oa Klinefelter Syndrome Information & Support. Tataiso ea Klinefelter Syndrome (pampiri ea PDF). Letsatsi la ho qetela le tsosolositsoeng: 2005. Tataiso ea Klinefelter Syndrome