Cyclic neutropenia ke boemo boo motho a bo futsitseng moo palo ea neutrophil (sele e tšoeu ea mali e loantšang maloetse a baktheria) e theoha haholo (hangata lisele tse ka tlaase ho 500 / mL) ho potoloha hoo e batlang e le matsatsi a 21 ohle. Hangata e fana ka selemo sa pele sa bophelo. Maqhubu a fokotseha ha a e-na le lilemo 'me a ka nyamela ho bakuli ba bang ba baholo.
Matšoao ke afe?
Ha palo ea neutrophil e tloaelehile, ha ho matšoao.
Matšoao a atisa ho hlaha ka mor'a neutropenia (palo e tlaase ea neutrophil) e bolelang hore palo ea neutrophil e se e le tlase haholo ka matsatsi a seng makae pele ho nts'etsopele ea matšoao. Ho hanyetsa mefuta e meng ea lefu la neutropenia (lefu le matla la congenital, Shwachman Diamond Syndrome , joalo-joalo), litšenyehelo tsa tsoalo ha li bonoe. Matšoao a kenyeletsa:
- Aphthous ulcers (likokoanyana tse molomong)
- Ho ruruha ho matla (pharyngitis)
- Gum ho ruruha (gingivitis)
- Matšoao a letlalo
- Feberu
Ke Mang ea Kotsing?
Cyclic neutropenia e bolela hore motho o tsoaloa a e-na le boemo. E fetisetsoa malapeng ka mokhoa o ikhethileng oa bo-autosomale e bolelang hore motsoali a le mong feela o lokela ho ameha ha a fetisetsa ho bana ba bona. Hase litho tsohle tsa lelapa tse ka 'nang tsa ameha ka tsela e tšoanang' me tse ling li ka 'na tsa e-ba le matšoao a mang feela.
E Tsejoa Joang?
Cyclic neutropenia e ka ba phephetso ho fumana hore na neutropenia e matla e nka matsatsi a 3 ho isa ho a 6 nakong ea potoloho ka 'ngoe.
Har'a lipallo tsena, lintlha tsa neutrophil li tloaelehile. Matšoao a molomo a tloaelehileng le feberu matsatsi ohle a 21 ho ea ho a 28 a lokela ho hlahisa lipelaelo bakeng sa neutropenia ea li-cyclic. E le ho tšoara potoloho ea neutropenia e matla, litlaleho tse feletseng tsa mali (CBC) li etsoa ka makhetlo a 2 ho isa ho a 3 ka beke libeke tse 6 ho isa ho tse 8.
Ho phaella ho neutropenia e matla, ho ka ba le ho fokotseha ha lisele tse khubelu tsa mali (reticulocytopenia) le / kapa platelets (thrombocytopenia).
Palo ea monocyte (mofuta o mong oa sele e tšoeu ea mali) hangata e eketseha nakong ea neutropenia e matla.
Haeba ho belaelloa hore ho na le li-neutropenia tsa li-cyclic ho latela likarolo tse ngata tsa mali, tlhahlobo ea liphatsa tsa lefutso e lokela ho romeloa ho batla liphetoho tsa ELANE gene (ka chromosome 19). Batho ba 90 - 100% ba nang le neutropenia ea cyclic ba na le phetoho ea ELANE. Liphetoho tsa lefutso liphatseng tsa lefutso tsa ELANE li amahanngoa le neutropenia ea li-cyclic le li-neutropenia tse matla haholo. Ka lebaka la tlhahiso ea litšebeletso le tlhahlobo ea liphatsa tsa lefutso, mesifa ea bone e sa hlokahale empa e atisa ho etsoa nakong ea mosebetsi oa neutropenia.
Litsela tsa Ts'ebetso ke life?
Le hoja neutropenia ea cyclic e nkoa e le boemo bo nang le bokooa, lefu la bobeli le mafu a tebileng le hlahile. Kalafo e reretsoe ho thibela le / kapa ho phekola mafu.
- Sebopeho sa Granulocyte Colony-Stimulating (G-CSF, e boetse e bitsoa filgrastim): G-CSF e susumetsa mokoallo oa masapo ho hlahisa li-neutrophils tse eketsehileng. E sebelisetsoa ho thibela palo ea neutrophil ho tloha ho theoha ka tlase ho lisele tse 500 / mL. G-CSF e bontšitsoe ho fokotsa matla a neutropenia le ho theola palo ea mafu a tšoaetsanoang. G-CSF e tsamaisoa ka tlas'a letlalo (ka tlasa letlalo) letsatsi le leng le le leng ho ea ho matsatsi a 2. Bakuli ba bang ba ka khona ho khaotsa G-CSF e le batho ba baholo hobane ka linako tse ling neutropenia e qala ho ba le bothata ba lilemo.
- Tlhokomelo ea meno e thibelang menyetla: Hobane mafu a mangata a hlaha molomong, ke habohlokoa ho boloka bohloeki bo botle. Moriana oa antibacteria o ka khothaletsoa.
- Hlahloba ka feberu: Hobane bakuli ba nang le neutropenia ba ka ba le tšoaetso e matla ea baktheria, ke habohlokoa hore likarolo tsa feberu li hlahlojoe ka hloko. Ka nako e 'ngoe, lihlopha tsena li tla hloka li-hospitalization tse nang le lithibela-mafu tse se nang tšoaetso (IV) ho fihlela tšoaetso e tebileng e ka felisoa.