POEMS syndrome ke lefu la mali le amang likarolo tse ngata tsa 'mele' me le baka matšoao a mangata. E ama banna le basali mme hangata e qala ka mor'a lilemo tse 50, le hoja e ka etsahala ka nako efe kapa efe. Ha ho tsejoe hantle hore na hangata lefu la POEMS le etsahala joang hobane ho thata ho fumana hore na le nepahetse hakae. Lebaka ha le tsejoe.
Matšoao
Seemahale POEMS se emela:
- P - polyneuropathy, e bolelang matšoao a matšoao a kang ho senyeha, ho lla, le / kapa bofokoli ba matsoho le maoto
- O - litho tse ling tse atolositsoeng, hangata sebete, spleen kapa lymph nodes. Hoo e ka bang karolo ea 15 lekholong ea batho ba nang le lefu la POEMS ba na le boloetse ba Castleman (lefu la lymph node disorder).
- E - endocrinopathy, e bolelang ho fetoha ha tlhahiso ea lihomone. Matšoao a kang lefu la tsoekere , ho hloka matla , ho khaotsa ho ea khoeling ( amenorrhea ), maemo a tlaase a qoqotho (hypothyroidism), le / kapa nts'etso-pele ea banna (gynecomastia) e ka ba teng.
- M - monomlonal gammopathy kapa boloetse bo bongata ba phallo ea mali e monoclonal, bobeli bo bolelang hore li-protheine tsa mali tse sa tloaelehang
- S - letlalo le fetoloa joalo ka ho eketsa letlalo la letlalo (hyperpigmentation); ho ba le moriri o moholo oa 'mele (hypertrichosis) sefahlehong, maotong le sefubeng; letlalo le tlala le ho tiisa, ho ruruha (edema) ea maoto le maoto, ho soeufala ha lipekere.
Batho ba ka 'na ba boela ba ba le bothata, mokhathala, mahlaba le bohloko bo tloaelehileng, kapa liphetoho ponong, har'a matšoao a mang.
Tsejoa
Ho fumanoa ke lefu la POEMS ho ka etsoa ho itšetlehile ka tlhahlobo ea mokuli le histori ea hae ea bongaka. Liteko tsa mali tse kang palo e feletseng ea lisele tsa mali (CBC) le serumprotein immunoelectrophoresis li etsoa ho sheba lintho tse sa tloaelehang, joalo ka ho hlahlojoa ha motsu. Matšoao a lihomone tsa qoqotho, litekanyo tsa tsoekere ea mali le litekanyetso tsa estrogen maling li lekoa ho lemoha ho se tloaelehe.
Motsoako oa masapo le / kapa lesapo x-ray li ka etsoa ho thusa ho hlahlojoa.
Motho o nkoa a e-na le lefu la POEMS haeba "P" (polyneuropathy) le "M" (e sa tloaelehang ea liprotheine tsa mali) li teng hammoho le lisele tsa scnerotic (scarring) bone kapa Castleman. Batho ba bangata ba tla ba le matšoao a mang a lefu lena. Hobane lingaka tse ngata ha li tsebe lefu la POEMS, liphello tse sa tloaelehang tsa tlhahlobo ea mali hangata li fella ka hore motho a se ke a tseba hore na ho na le mefuta e mengata ea myeloma, kapa matšoao a polyneuropathy a lebisa tlhokomelo e fosahetseng ea boloetse bo sa foleng ba ho ruruha ho matla ha motlakase (CIDP).
Phekolo
Phekolo ea lefu la POEMS e itšetlehile ka phekolo ea lefu la sele ea mali. Batho ba bangata ba fumana mefuta e meng ea phekolo e kang:
- Phekolo ea meriana
- Meriana ea Corticosteroid e kang prednisone
- Chemotherapy
- Hormone phetolo ea lihomone tse tlase haholo
- Phekolo ea 'mele
- Transplant ea bone ea 'mele
Lingaka tse kang ngaka ea methapo ea mafu (methapo ea methapo ea mafu), lefu la hematologist (ngaka ea mafu a mali), dermatologist (ngaka ea letlalo) le setsebi sa endocrinologist (hormone gland doctor) hangata se ameha ho tlhokomelong ea motho ea nang le lefu la POEMS.
Lisebelisoa:
Dispenzieri, Angela. "POEMS Syndrome." Hematology 2005 (2005): 360-367.
Angela R. Kyle, Martha Q. Lacy, S. Vincent Rajkumar, Terry M. Therneau, Dirk R. Larson, Philip R. Greipp, Thomas E. Witzig, Rita Basu, Guillermo A. Suarez, Rafael Fonseca, John A. Lust, & Morie A. Gertz. "TŠEBELETSO EA BOPHELO: litlhaloso le liphello tsa nako e telele." Mali 101 (2003): 2496-2506.
"Matšoao a POEMS Syndrome." Kalafo ea POEMS Syndrome ho Mayo Clinic. Mayo Clinic. 22 Mantaha 2007
Chan, Joanna, & Wingfield Rehmus. "POEMS Syndrome." eMedicine. 15 Dec 2006. WebMD. 22 Mantaha 2007