E sa ntse e le sephiri, sarcoidosis ke boloetse bo sa tsejoeng - le hoja tšoaetso ea 'mele ea ho itšireletsa mafung le maikutlo a motho ea ho itšireletsa mafung a lumela hore ke a bohlokoa. Sarcoidosis, ka nako e 'ngoe e bitsoa sarcoid feela, e lebisa mofuteng oa ho ruruha o bonahalang tlas'a microscope mme e ka ama likarolo tse fapaneng tsa' mele. Sarcoidosis e ka ama setho leha e le sefe, empa ho ka etsahala hore se ama litssaete tse latelang:
- Lung
- Letlalo
- Lymph nodes - haholo-holo lymph nodes ka sefubeng
Sarcoidosis e boetse e tsebahala ka matla a eona a ho ama mahlo le sebete. Ntho e sa tloaelehang, pelo le boko li ka 'na tsa ameha, tse lebisang mathateng a tebileng.
Ho ea ka pono ea lisele le mahlaseli, pontšo ea sarcoidosis ke ntho e bitsoang granuloma. Li-granulom li bokellana le lisele tseo, tlas'a microscope, li shebahala li tšoana haholo le tseo 'mele o li sebelisang ho loantša mafu a kang lefuba.
Hase bohle ba nang le sarcoidosis ba hlokang phekolo, mme hangata e fela ntle le phekolo, empa maemong a mang, e ka baka mafu a maholo. Ha litho tsa 'mele li ameha, mohlala, lithethefatsi tse sa tšoaneng tse etselitsoeng ho thibela sesole sa' mele li ka sebelisoa.
Matšoao a ka 'na a amana le litho tse amehang ho lefu lena, kapa ho ka' na ha e-ba le matšoao a tloaelehileng a kang mokhathala, feberu, ho ruruha lymph nodes, le ho lahleheloa ke boima ba 'mele . Ho kenyeletsa likokoana-hloko ho tloaelehile haholo 'me matšoao a ka' na a kenyelletsa ho khohlela ho omeletseng ho tsitsitseng, phefumoloho e khutšoanyane, bohloko ba sefuba kapa sefuba.
Batho ba bang ba nang le sarcoidosis ba hlaolela matšoao a letlalo a kang lehare le entsoeng ka li-bumps tse khubelu kapa tse lefifi tse khubelu.
Lymphoma
Lymphoma ke e 'ngoe ea "kankere ea mali," kapa likokoana-hloko tsa hematologic, e leng lentsoe le akarelletsang leukemias le myeloma . Lymphoma ke kankere ea lisele tsa mali tse tšoeu tsa lymphocyte. Ho na le mefuta e fapaneng ea lymphoma.
Tse ngata, empa eseng tsohle, lymphomas li qala ka lymph nodes.
Likarolo tse peli tse sephara tsa lymphoma ke Hodgkin (HL) le non-Hodgkin (NHL) lymphoma. Likarolo tsena ka bobeli li na le mefuta e mengata le likaroloana tse ka hare, tse nang le likarolo tse fapaneng tsa lefu le li-prognoses.
Hodgkin le non-Hodgkin lymphoma li ka ama lymph nodes tsa sefubeng - sebaka se haufi le pelo e bitsoang mediastinum. Sarcoidosis e boetse e akarelletsa sebaka sena.
Sarcoidosis le Lymphoma
Ka lilemo tse mashome, bafuputsi ba ipotsa hore na kamano e teng pakeng tsa sarcoidosis le lymphoma. Kamano ena e ntse e makatsa esita le kajeno, ka mabaka a 'maloa.
Ho ea ka sehlopha sa bafuputsi ba akarelletsang Ishida le basebetsi-'moho le bona, "Thepa e tloaelehileng haholo ea malignant lymphoma e amanang le sarcoidosis ke Hodgkin lymphoma, empa boholo ba B-cell lymphoma, follicular lymphoma le myeloma e mengata e ka boela ea kenella sarcoidosis-lymphoma syndrome. "Lentsoe" Sarcoid-lymphoma syndrome "le ne le sebelisitsoe ho hlalosa lintho tsena tse fumanoeng.
Li-granulomas tse hlaheletseng tsa sarcoidosis li kopane, li hlophisitsoe li hlophisitsoeng tsa lisele tsa 'mele tsa ho itšireletsa mafung tse pota-potiloeng ke lymphocytes. Kamoo ho bonahalang kateng, lymphomas ka linako tse ling e ka tšoara "granulomas" ka har'a kankere - 'me phetoho ena, le hoja e le e sa tloaelehang, ho nahanoa hore mohlomong e bonahatsa tšoaetso ea' mele ea ho itšireletsa mafung le kankere ea kankere, eseng lefu la systemic, sarcoidosis.
Litokomane tse phatlalalitsoeng lilemong tse 'maloa tse fetileng li hlokometse hore ho khetholla pakeng tsa likarabo tse amanang le lithethefatsi le' nete ea systemic sarcoidosis e ka 'na ea e-ba bothata.
Bobeli ba sarcoidosis le lymphoma ba na le monyetla oa ho "khantša" ho PET ho hlahloba, ho eketsa ho rarahaneng le ho khoneha bakeng sa ntho e ferekanyang ho e 'ngoe. Bafuputsi ba batla lithuto tse eketsehileng ho ntlafatsa lik'hamphani tsa lik'hamphani tsa FDG-PET / CT ho bakuli ba nang le sarcoidosis.
Ka bokhutšoanyane, lipotso tse ngata mabapi le sarcoidosis-lymphoma syndrome ha li na karabo.
> Mehloli:
Ishida M, Hodohara K, Furuya A, et al. Li-granulomas tse nang le li-granulomas li-lymph nodes ka mor'a hore li phekoloe sebakeng sa marginal zone lymphoma ea sekhahla: tlaleho ea nyeoe ka ho hlahloba maikutlo a sarcoidosis-lymphoma syndrome. Int J Clin Exp Pathol . 2014; 7 (7): 4428-4432.
Mellemkjaer L, Pfeiffer RM, Mantsoe EA EA, Gridley G, Wheeler W, Hemminki K, Olsen JH, Dreyer L, Linet MS, Goldin LR, Landgren O. Ho itšireletsa mafung ho batho ka bomong le ho litho tsa malapa a haufi le ho amoheloa ke li-lymphoma tseo e seng tsa Hodgkin. Ramatiki ea Rheum . 2008; 58: 657-666.
Jen Reich JM, Mullooly JP, Johnson RE. Tlhahlobo ea ho kopanya li-sarcoidosis tse amanang le malign. Sefuba. 1995; 107: 605-613
National Heart Lung le Blood Institute. Sarcoidosis ke Eng? E fihlile ka January 2016.
Goswami T, Siddique S, Cohen P, Cheson BD. Sarcoid-lymphoma syndrome. Clin Lymphoma Myeloma Leuk . 2010; 10: 241-247.