Na Meriana e meng e ka U thusa ho Laola Muscular Dystrophy?

Likgetho tsena tse kotsing tse ka bang kotsi li ka etsa phapang e ntle

Ho senyeha ha mesifa ke sehlopha sa mathata a liphatsa tsa lefutso tse bontšitsoeng ke bofokoli bo tsoelang pele, ho senya le ho senyeha ha mesifa ea masapo e laolang ho tsamaea. Ha ho na phekolo e tsebahalang bakeng sa ho ruruha ha mesifa, 'me hangata bakuli ba retelehela meriana e meng ea ho phekola lefu lena.

Matšoao a Tlhaho bakeng sa Muscular Dystrophy

Ho tla fihlela joale, liphuputso tse fokolang li 'nile tsa lekola tšebeliso ea meriana e meng ea phekolo bakeng sa phekolo ea mesifa ea dystrophy .

Leha ho le joalo, ho na le bopaki bo bong ba hore mofuta o mong oa mefuta e meng ea phekolo e ka fana ka melemo ho bakuli ba meriana ea boloetse ba mahlaba, le hoja boholo ba lithuto li se li le moholo. Mona ho sheba liphuputso tse 'maloa tsa thuto:

1) Lijo tse ling tsa lijo

Liphuputso tse 'maloa tse nyenyane li bontša hore lijo tse ling tsa lijo li ka thusa basebeletsi ba meriana ea ho itšireletsa mafung. Ka mohlala, phuputso e entsoeng ka 2006 ho American Journal of Clinical Nutrition e fumane hore tlatsetso ea li-amino acid e thusitse ho thibela ho felisoa ha liprotheine tsa 'mele (e leng sekheo sa Duchenne muscular dystrophy). Thuto ena e ne e akarelletsa bashanyana ba 26 ba nang le Duchenne muscular dystrophy, e mong le e mong oa bona ea neng a phekoloa ka amino acid bakeng sa matsatsi a 10.

Phuputso ea pele e boetse e bontša hore sebōpeho (e leng amino acid e thusang ho fana ka lisele tsa mesifa le matla) e ka 'na ea thusa ho tšoara lefu la mesifa ea mesifa. Leha ho le joalo, ka phuputso ea 2005 ea bashanyana ba 50 ba nang le Duchenne muscular dystrophy (e phatlalalitsoeng ho Annals of Neurology ), bo-rasaense ba fumane hore likhoeli tse tšeletseng tsa kalafo ka lisebelisoa tsa creatine li hlōlehile ho ntlafatsa matla a mesifa ho barupeluoa.

2) Qigong

Qigong e ka ntlafatsa bophelo bo botle ho batho ba nang le mesifa ea ho senyeha ha mesifa, ho ea ka phuputso ea 2004 e hatisitsoeng ka bokooa le bofetoheli. Thuto ena e ne e kenyeletsa bakuli ba 28 ba nang le boloetse ba ho senyeha ha mesifa, bao ba bang ba bona ba ileng ba tlaleha ntlafatso ea boiketlo ba kelello, 'meleng le kelellong (ntle le ho fokotseha ha maemo a khatello ea kelello) ka mor'a ho qigong.

3) Tea e Tala

Tee e tala e ka ba molemo ho batho ba nang le Duchenne muscular dystrophy, ho ea ka lipatlisiso tsa pele tse phatlalalitsoeng American Journal of Physiology: Cell Physiology ka 2006. Ha ho etsoa tlhahlobo ho litoeba, bafuputsi ba fumane hore epigallocatechin gallate (antioxidant e fumanoang ka tee e tala) e ka ' thusa ho sireletsa khahlanong le ho senyeha ha mesifa ho bakoang ke ho senyeha ha mesifa. Leha ho le joalo, haufinyane ho tla tseba hore na green tea e ka ba le phello e tšoanang ho batho.

Mefuta ea Muscular Dystrophy

Ho na le maloetse a fetang 30 a khetholloang e le mesifa ea 'mele. Le hoja mefuta e meng e hlaha ho tloha boseeng kapa bongoaneng, tse ling ha li bonoe ho fihlela lilemong tsa bohareng kapa hamorao bophelong. Lintho tse kang lilemo tsa ts'ebetso, bofokoli ba mesifa, le tekanyo ea tsoelo-pele e fapana ho latela mofuta oa mesifa ea dystrophy.

Tsela e tloaelehileng ka ho fetisisa ea ho ruruha ha mesifa e tsebahala e le Duchenne muscular dystrophy. E ama bashanyana haholo, Duchenne muscular dystrophy e bakoa ke ho ba sieo ha dystrophin (protheine e phethang karolo ea bohlokoa ho boloka botšepehi ba mesifa). Ho fokola ha mesifa ho tloaelehile ho hlaha pakeng tsa lilemo tse tharo le tse hlano, hangata ho siea bakuli ba sitoang ho tsamaea ka lilemo tse 12.

Mefuta e meng ea mesifa ea ho senyeha ha mesifa e akarelletsa facioscapulohumeral muscular dystrophy (e tšoaeang ke bofokoli bo tsoelang pele ba mesifa, matsoho, maoto le mahlakoreng le sefubeng) le myotonic muscular dystrophy (e tšoauoeng ke ho fokola ha mesifa, nako e telele, ho se tšoane ha pelo le ho senyeha ha endocrine ).

Matšoao le Matšoao a Muscular Dystrophy

Matšoao a mesifa ea dystrophy e fapana ho ea ka mofuta oa mesifa ea masapo. Ka mohlala, matšoao a Duchenne muscular dystrophy a ka kenyelletsa ho lieha ho tsamaea ka likoloi, ho oa ka makhetlo a mangata, ho fokola meleng e ka tlase, mesifa e khōlō ea namane le ho senyeha ha mohopolo. Bothata ba ho senyeha ha mesotonic, nakong e sa lekanyetsoang, ho ka baka matšoao a kang bofokoli maotleng a sefahleho (hammoho le matsohong le maotong le mesifa e amang puo le ho metsa), ho beola, mathata a ho hema, le ho se tloaelehe ha pelo ha motho a le moholo.

Phekolo ea Muscular Dystrophy

Kalafo bakeng sa ho senyeha ha mesifa e atisa ho akarelletsa phekolo ea meriana, phekolo ea ho phefumoloha , phekolo ea puo , lisebelisoa tsa meriana tse sebelisetsoang ho tšehetsa, le ho buuoa ka masapo .

Meriana e meng e boetse e sebelisoa ho sebetsana le ho bolaoa ke mesifa, ho akarelletsa le corticosteroids (ho fokotsa mesifa ea ho fokola), li-anticonvulsants (ho thibela ho tsuba le ho etsa lintho tse ling tsa mesifa), li-immunosuppressants (ho liehisa tšenyo e itseng ho lisele tsa mesifa), le lithibela-mafu (ho loantša mafu a tšoaetso) .

Maemong a mang, bakuli ba mesifa ba nang le mesifa ba ka 'na ba hloka ho thusoa ke moea (ho phekola bofokoli ba mesifa) le / kapa pacemaker (ho tšoara bobebe ba pelo).

Ho Sebelisa Meriana e Meng ea Meriana bakeng sa Muscular Dystrophy

Haeba u nahana ka tšebeliso ea mefuta efe kapa efe ea meriana e meng ea phekolo ea meriana ea lefuba, ke habohlokoa hore u buisane le ngaka ea hao (kapa ngoana oa ngoana oa hao) pele o qala kalafo. Ho ikoetlisa ha mesifa le ho phekola meriana e meng ho itlhokomela ho ka ba le liphello tse tebileng.

> Mehloli:

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> DM Escolar, Buyse G, Henricson E, Leshner R, Florence J, Mayhew J, Tesi-Rocha C, Gorni K, Pasquali L, Patel KM, McCarter R, Huang J, Mayhew T, Bertorini T, Carlo J, Connolly AM , Clemens PR, Goemans N, Iannaccone ST, Igarashi M, Nevo Y, Pestronk A, Subramony SH, Vedanarayanan VV, Wessel H; Sehlopha sa CINRG. "CINRG Tlhahlobo e laoloang e laoloang ea Creatine le Glutamine ho Duchenne Muscular Dystrophy." Ann Neurol. 2005 Jul; 58 (1): 151-5.

> Felber S, Skladal D, Wyss M, Kremser C, Koller A, Sperl W. "Oral Creatine Supplementation in Duchenne Muscular Dystrophy: Thuto ea K'homphieutha le ea 31 Magnetic Resonance Study Spectroscopy." Neurol Res. 2000 Mar; 22 (2): 145-50.

> E-E, Eléouet-Da Violante C, > Sefuba > C, Gottrand F, Rigal O, Fontan JE, Cuisset JM, Guilhot J, Hankard R. "Oral Glutamine le Amino Acid Supplementation li thibela ho silafatsa liprotheine tsa bana ba nang le Duchenne Muscular Dystrophy. " Am J Lijoana tsa Mmele. 2006 Mar; 83 (4): 823-8.

> Nabukera SK, Romitti PA, Campbell KA, Meaney FJ, Caspers KM, Mathews KD, Hokert Sherlock SM, Puzhankara S, Cunniff C, Druschel CM, Pandya S, Matthews DJ, Ciafaloni E, Starnet M. "Tšebeliso ea Tlatsetso le Mokhoa o Mong Meriana e Tona ea Basona le Duchenne kapa Becker Muscular Dystrophy. " J Child Neurol. 2011 ka 7.

> Setsi sa Sechaba sa Mathata a Ts'oaetso le Lefu. "Boitsebiso ba Muscular Dystrophy Page." La 14 November, 2011.

> Pearlman JP, RA Fielding. "Creatine Monohydrate e le Thuso ea Meriana ho Muscular Dystrophy." Tlhahiso ea lihlahisoa ka 2006 Feb; 64 (2 Pt. 1): 80-8.

> Wenneberg > S, Gunnarsson LG, Ahlström G. "Ho sebelisa Lenaneo la ho ikoetlisa le Machaba bakeng sa bakuli ba nang le Muscular Dystrophy Karolo ea I: Thuto e Tšoanelehang." Khutlisetsa Bofetoheli. 2004 ka 20, 20; 26 (10): 586-94.