Bartter Syndrome

Maloetse a liphio a futsanehileng

Bothata ba Bartter ke lefu le nang le lefu la liphio le nahanang hore le bakoa ke bokooa ha bophio bo khona ho khutlisetsa potassium. Sena se etsa hore liphio li tlose potasiamo e ngata haholo 'meleng.

Matšoao a Bartter a futsitse ka mokhoa o ikemetseng oa boipheliso , le hoja ka linako tse ling ho ka etsahala ho motho ea se nang histori ea lelapa ea lefu lena. Ha ho tsejoe hantle hore na kankere ea Bartter e atisa ho etsahala joang, empa phuputso e 'ngoe e hakanya hore e ama batho ba 1.2 ho batho ba limilione.

Ho bonahala eka ho etsahala hangata ho bana ba tsoaloang ke batsoali ba nang le mekhoa e metle, kapa ba amanang haholo. Lefu la Bartter le ama banna le basali ba merabe eohle.

Matšoao

Matšoao a lefu la Bartter a ka 'na a akarelletsa:

Bana ba nang le lefu la Bartter ba thatafalloa ke ho hōla le ho ba le maemo a tloaelehileng.

Tsejoa

Matšoao a Bartter a atisa ho fumanoa a sa le banyenyane ho itšetlehile ka tlhahlobo ea 'mele, matšoao a teng, le liphello tsa liteko tsa mali le lisele tsa laboratory. Tsena li kenyelletsa:

Gitelman syndrome e tšoana le lefu la Bartter e le hore ho ka hlokahala liteko tse eketsehileng ho fumana hore na ke lefu lefe le teng.

Phekolo

Phekolo ea lefu la Bartter e lebisa tlhokomelo ea ho boloka potassiamo ea mali ka mokhoa o tloaelehileng. Sena se etsoa ka ho ba le lijo tse nang le potassium le ho nka li-supplementum tsa potassium ha ho hlokahala. Hape ho na le lithethefatsi tse fokotsang tahlehelo ea potasiamo meleng, e kang spironolactone, triamterene, kapa amiloride.

Meriana e meng e sebelisetsoang ho tšoara lefu la Bartter e ka kenyelletsa indomethacin, captopril, le bana, ho hōla ha hormone.

> Mehloli:

> "Bartter Syndrome." Medical Encyclopedia. 15 Oct 2008. MedlinePlus.

> "Bartter's Syndrome ke eng?" Lihlooho. 5 Mphalane 2008. The Bartter Site.

> "Bartter Syndrome." Matšoafo a li-tubula le a mafu a likokoana-hloko. Dec 2006. The Merck Manuals Medical Online Library.