Mofuta oa Arthritis le Sebōpeho sa Tsamaiso ea Vasculitis
Boloetse ba Kawasaki ke e 'ngoe ea mefuta e fetang 100 ea ramatiki, ho ea ka Arthritis Foundation. Matšoao a Kawasaki ke mofuta oa mesifa e tloaelehileng e hlahisang bana ba banyenyane; Bacha ba 80% ba Kawasaki ba ka tlase ho lilemo tse 5.
Tomasaku Kawasaki o ile a qala ho tseba lefu lena ka 1967 Japane. Pele e khethoa e le lefu la Kawasaki, boemo boo bo ne bo tsejoa e le lefu la lymph node la mucocutaneous.
E boetse e bitsoa boloetse ba Kawasaki, Kawasaki's syndrome le infantile polyarteritis.
Matšoao
Phofo ea Kawasaki e ka amahanngoa le ntshetsopele ea coronary arteritis (ho ruruha ha methapo ea coronary) le ho thehoa ha li-aneurysms. United States, lefu la Kawasaki le nkoa e le sesosa se ka sehloohong se bakoang ke lefu la pelo ho bana.
Matšoao a Kawasaki a qala ka potlako 'me a qeta libeke tse ngata a le mabifi. Ka tloaelo, boemo boo bo rarolla. Leha ho le joalo, e rarolla mathata a pelo ka mor'a lilemo.
Matšoao a mang a amanang le mafu a Kawasaki a kenyelletsa:
- feberu e fokolang e qetellang matsatsi a 5 kapa ho feta (ho hlokehang ho etsa hore ho fumanoe mafu a Kawasaki)
- mahlo a masoabi (mahlo) a se nang pus
- melomo e khubelu
- khubelu e khubelu molomong
- leleme le khubelu le nang le ponahalo ea fragola
- li-rashes holim'a kutu ea 'mele
- liphaphatha tse khubelu tsa matsoho le maoto a khubelu a maoto
- edema ea matsoho le maoto
- ho senya letlalo matsohong, maotong, le liphatsa tsa lefutso
- ho ruruha ha lymph node hangata haufi le molala
- ho utloa bohloko le ho ruruha hangata mahlakoreng ka bobeli a 'mele
Liphuputso tse ling tse sa tloaelehang tse ka hlahang ka lefu la Kawasaki li kenyelletsa aseptic meningitis, pyuria e nyenyane le urethritis, letšollo, mahlaba a mpeng, phallo ea mahlaba, ho thibela malapa, le li-hydrops tsa gallbladder.
Lebaka
Ba bang ba belaella hore ho na le sesosa se tšoaetsanoang sa lefu la Kawasaki, empa ha ho le bopaki bo bontšitsoeng. Ho na le mekhoa e 'maloa ea li-immunologic tse amanang le boloetse ba Kawasaki,' me ba bang ba lumela hore ke boemo bo ikemetseng .
Ho ata
United States, lefu la Kawasaki le ama bana ba 4 000 selemo le selemo. E atile haholo Japane moo e fumanoeng ka linyeoe tse 5 000 ho isa ho tse 6 000 selemo le selemo.
Litlhare
Hang ha lefu lena le fumanoa, phekolo e potlakileng e khothalletsoa e le hore tšenyo ea methapo ea pelo le pelo e ka thibeloa. The immune globulin (IVIG) e fokolang e fumanoang ka tekanyo e phahameng e nkoa e le phekolo e tloaelehileng ea lefu la Kawasaki. Semasine e phahameng ea aspirin e atisa ho ba karolo ea morero oa phekolo. Hangata li-glucocorticoids ha li sebelisoe ho phekola lefu la Kawasaki.
Ka phekolo ea pele bakeng sa lefu la Kawasaki, ba bangata ba ka khona ho hlaphoheloa ka botlalo, empa ba 2% ba bakuli ba lefu la Kawasaki ba shoa ka mathata a ho ruruha ha methapo ea mali. Ho khothalletsoa hore bakuli ba nang le lefu la Kawasaki ba na le EKG (echocardiogram) lilemo tse peli kapa tse peli ho hlahloba mathata a pelo a setseng.
Lisebelisoa:
Vasculitides. Maloetse a Kawasaki (Khaolo ea 21). Primer ka Rheumatic Diseases . Khatiso ea 13. E phatlalalitsoe ke Arthritis Foundation. Klippel J. et al.
Hase Feela Bohloko bo Hōlang . Maloetse a Kawasaki Khaolo ea 17. Thomas JA Lehman, MD. Oxford University Press. 2004.
Maloetse a Kawasaki. MedlinePlus. NLM le NIH. 11/29/2006.