Lefu la Matšoao a Aparelang
Matšoao a macha a metsoako (MCTD) ke boloetse bo ikemetseng ba likokoana-hloko tse nang le likarolo tse ling tse tharo tsa mafu a maiketsetso- lipilisi tsa lupus erythematosus , scleroderma le polymyositis.
Lebaka
Lebaka la MCTD ha le tsejoe. Hoo e ka bang karolo ea 80 lekholong ea batho ba fumanoang ba e-na le MCTD ke basali. Lefu lena le ama batho ba lilemo li 5 ho ea ho tse 80 le ho feta ha bacha kapa batho ba lilemong tsa bo-20.
E ka 'na eaba ho na le liphatsa tsa lefutso empa ha li futsane ka ho toba.
Matšoao
Matšoao a mathomo a mafu a maiketsetso a maiketsetso a tšoana le matšoao a amanang le maloetse a mang a maiketsetso 'me a kenyeletsa:
- Mokhathala
- Bohloko ba mesifa kapa bofokoli
- Mahlaba a kopantsoeng
- Feberu e tlaase
- Ketsahalo ea Raynaud
Matšoao a seng makae a tloaelehileng a amanang le MCTD a kenyeletsa matla a li-polymyositis (boholo a amanang le mahetla le matsoho a ka holimo), bohloko ba ramatiki a maholo, aseptic meningitis, myelitis, likoboana tsa menoana le menoana, mahlaba a phahameng, mahlaba a mpeng, neuropathy ea methapo ea thobalano sefahlehong, ho thata ho emisa, phefumoloho e khutšoanyane le ho lahleheloa ke kutlo. Matšoafo a ameha ho batho ba etsang karolo ea 75 lekholong ba nang le MCTD. Hoo e ka bang karolo ea 25 lekholong ea bakuli ba nang le MCTD ba na le karolo ea liphio.
Tsejoa
Ho lemoha mafu a maiketsetso a tsoakaneng ho ka ba thata haholo. Likarolo tsa maemo ana a mararo-lupus erythematosus e sebetsang ka tsela e tloaelehileng, scleroderma le polymyositis-hangata ha e hlahe ka nako e le 'ngoe.
Ho e-na le hoo, hangata ba hlaolela e mong ka mor'a nako e 'ngoe.
Leha ho le joalo, ho na le lintlha tse 'nè tse ka bontšang hore motho o tšoeroe ke MCTD ho e-na le ho kula ha motho ka mong:
- Mokhoa o phahameng oa anti-U1 RNP (ribonucleoprotein) maling
- Ho ba sieo ha mathata a itseng a tloaelehileng le tsamaiso ea lupus erythematosus, e kang mathata a liphio le mathata a mangata a tsamaiso ea methapo
- Matšoao a matla a masapo le mali a mokuli (a sa tloaelehang ka systemic lupus kapa scleroderma)
- Ketsahalo ea Raynaud, le matsoho a ruruhileng (a sa tloaelehang le systemic lupus)
Le hoja boteng ba anti-U1 RNP e le tšobotsi e ka sehloohong e khethollang ho tseba hore na MCTD e na le eng, ho ba teng ha anti-oela ka mali ho ka lebisa matšoao.
Phekolo
Kalafo ea mafu a tsoekere a tsoekere a ikemiselitse ho laola matšoao le ho sebetsana le liphello tse matla tsa lefu lena, joalo ka ho ameha ha setho. Ka mohlala, khaello ea meriana ea mali e lokela ho phekoloa ka meriana e loantšang mali. Matšoao a ho ruruha a ka 'na a hlaha ho tloha bofokoling ho fihlela a le matla,' me kalafo e tla khethoa ho latela boima. Bakeng sa ho ruruha ho fokolang ho fokolang, li- NSAID kapa li- corticosteroids tse tlaase li ka fanoa. Ho tloaela ho ruruha ho matla ho ka 'na ha hloka hore ho be le lekhopho le phahameng la corticosteroids. Ha ho e-na le tšebetso ea litho, li-immunosuppressants li ka be li laeloa.
Outlook
Esita le ka ho hlahloba ka ho nepahetseng le kalafo e nepahetseng, ho ka ba thata ho etsa qeto ea hore na u tla etsa'ng. Mokuli o etsa hantle hakae ho itšetlehile ka hore na ke litho life tse amehang, ho teba ha ho ruruha le tsoelo-pele ea lefu lena. Ho latela Cleveland Clinic, karolo ea 80 lekholong ea batho e phela lilemo tse 10 ka mor'a hore ba fumanoe ba e-na le MCTD.
Tlhahiso ea MCTD e atisa ho ba mpe le ho feta ho bakuli ba nang le litšobotsi tse tlameletsoe ho scleroderma kapa polymyositis.
Ke habohlokoa ho hlokomela hore ho ka ba le nako e atolositsoeng e sa nang le matšoao, esita le ho se na phekolo ea MCTD.
> Mehloli:
> Bennett R. Anti-U1 RNP Likokoana-hloko Likokotlong Tse Tsitsitseng tsa Matšoao a Tisue. E maemong.
> Firestein GS, Kelley WN. Kelleys Textbook ea Rheumatology . Philadelphia, PA: Elsevier / Saunders; 2013.
> Gunnarsson R, Hetlevik SO, Lilleby V, Molberg Ø. Lefu le ferekanyang la mesifa. Mekhoa e metle ea ho etsa lipatlisiso le lipatlisiso tsa Rheumatology ea Clinic . 2016; 30 (1): 95-111. doi: 10.1016 / j.berh.2016.03.002.
> Mafu a Tšebelisano a Maiketsetso a Kopaneng. Cleveland Clinic.