Ho sebetsana le boemo ba Atlantoaxial Instability (AAI) ho Down Syndrome

AAI Sephetho se Tsoang ho Vertebrae e sa Tšoaneng

Ho se tsitse ha Atlantoaxial (AAI) ke bothata bo tloaelehileng ba masapo bo fumanoang ho batho ba nang le Down syndrome. Le hoja e e-na le lebitso le rarahaneng mme le utloahala eka le tšosoa, haholo-holo, le bakela ba nang le lona mathata. E le hore u utloisise AAI, ke habohlokoa hore u utloisise hanyenyane ka mosebetsi le mokhoa oa mokokotlo oa methapo ea methapo, methapo, li-vertebrae le li-ligaments.

Mokokotlo oa mokokotlo, Metsing, Vertebrae le Ligaments

Tlhōrō ea mokokotlo oa mokokotlo ke teteana e teteaneng-e kang sebopeho se qalang botong ba boko 'me se tsamaea hohle ho ea fihla sebakeng sa lumbar. Mohala oa mokokotlo o na le methapo ea mmele kapa li-neurons. Metsing ke mofuta o khethehileng oa sele e tsamaisang melaetsa pakeng tsa boko le 'mele oohle. Meriana e tšoana le mochine oa motlakase o fetang motlakase o nang le lipontšo pakeng tsa likarolo tsa 'mele.

Li-vertebrae li na le masapo a sa tšoaneng a hlophisehileng a hlophisitsoeng ka lehlakoreng le ka morao ho 'mele o tsoang botlaaseng ba boko ho ea pelong. Molamu oa mokokotlo o phalla 'me o sirelelitsoe ke botlalo ba li-vertebrae. Ho na le li-vertebrae tse 33, tse atisang ho aroloa libakeng tse 'nè: li-cervical (7), thoracic (12), lumbar (5) le vertebra ea pelvis. Li-vertebrae tsa mokokotlo li sebakeng sa molala 'me li khutsufatsoa joaloka C1-C7. Haeba o khumamela hlooho mme o matha menoana ka morao ho hlooho ea hau, botumo ba pele bo boholo boo u ikutloang ke C1 ea hau kapa vertebra ea mokokotlo.

E latelang e tlase ke C2 le tse ling tse joalo. C1 e bitsoa vertebra ea Atlas le C2 e le li-vertebra. Ho tlosoa hampe ha li-vertebrae ho bitsoa ho se tsitse ha atlantoaxial kapa AAI.

Li-vertebrae li tšoareloa libakeng le mesifa le li-ligaments. Mesebetsi ea lenane la lesapo la mokokotlo le akarelletsa ts'ireletso ea mokokotlo le litho tsa ka hare, tšehetso ea moralo bakeng sa hlooho le ho boloka maemo a mabeli le ho tsamaea.

Kaha batho ba nang le Down syndrome ba na le molumo o tlaase oa mesifa le li-lax ligaments, li-vertebrae tsa bona li ka senyeha hampe. Ha C1 le C2 vertebrae li sa tsamaisoe hantle, u na le AAI. Ho batho ba nang le Down syndrome, ligament e atisang ho ameha ho AAI e bitsoa "taelo e fetohang."

Tlhahlobo ea AAI

Maemo a mangata a ho tlosoa habonolo AAI a etsoa ka ho hlahloba x-ray. Bana bohle ba nang le Down syndrome ba lokela ho hlahlojoa ho AAI ka lilemo tse 3. Ho fumanoa ha matšoao a tšoaetso AAI hangata ho etsoa ka tlhahlobo ea methapo ea kutlo (tlhahlobo ea 'mele e hlahlobang kamoo methapo e sebetsang kateng) le / kapa ka x-ray.

Mefuta ea AAI

Ho na le mefuta e 'meli ea sekhahla sa atlantoaxial - asymptomatic AAI le matšoao a AAI. Asymptomatic AAI e bolela hore AAI e ka bonoa ka x-ray, empa ha e bake mathata leha e le efe a neurologic ho motho ea nang le eona. Symptomatic AAI e bolela hore AAI e teng ka x-ray, mme e baka mathata a mang a methapo ea pelo ho motho ea nang le eona. Batho ba pakeng tsa 10% ho isa ho 20% ba nang le Down syndrome ba na le mahlakore a mararo a AAI ka x-ray, 'me ke feela 1% ho 2% ea batho ba nang le Down syndrome ba nang le matšoao a tšoaetso AAI.

Matšoao a Neurologic a AAI

E 'ngoe ea mesebetsi ea lenane la ho qetela ke ho sireletsa mokokotlo oa mokokotlo, o tsamaeang ka hare ho oona.

Mokokotlo oa mokokotlo ke pokello ea methapo e sireletsoang ke molumo oa mahlo. Symptomatic AAI e baka matšoao a sa tšoaneng a methapo ea kelello e kang:

Haeba motho ea nang le Down syndrome a hlahisa leha e le efe ea matšoao ana a methapo ea pelo, ba lokela ho hlahlojoa hang-hang ke ngaka. Hangata ngaka e etsa tlhahlobo e feletseng ea methapo ea methapo le ho laola lithuto tsa ho etsa litšoantšo, tse kang x-ray, CT kapa MRI.

Phekolo ea AAI

Asymptomatic AA ha e hloke phekolo leha e le efe. Hangata batsoali ba mpa ba eletsoa hore na ke matšoao afe ao motho a ka e bonang ho motho ea nang le AAI.

Haeba motho a bontša matšoao a ho imeloa ha mokokotlo oa mokokotlo, phekolo e bontšoa. Lipakane tsa ho phekola matšoao a AAI ke ho sireletsa mokokotlo oa mokokotlo, ho tsitsisa khoele ea mokokotlo kapa vertebrae le decompress meroallo leha e le efe e sitetsoeng. Ho itšetlehile ka boholo ba bothata, ho tsitsisa mokokotlo oa mokokotlo ho ka finyelloa ka ho apara molaleng o bonolo, halter traction le meriana e utloisang bohloko le mesifa e phopholetsang 'me mohlomong ho buuoa.

Lisebelisoa:

Univesithi ea Amerika ea Pediatrics, Komiti ea Meriana ea Meriana. Atlantoaxial ho se tsitse ha Down syndrome. Lingaka. Moq. 107 No. 2, February 2001, maq. 442-449 [/]

Alvarez, N. Atlantoaxial Instability ho Batho ba nang le Down Syndrome, Emedicine , la 8 8, 2008.