Ho falla, ho leka-lekanya, le tsebo ea likoloi tse atisang ho ameha
Mokhoa o ka sehloohong oa multiple sclerosis (PPMS) o ama batho ba bangata ho ba robeli ba phelang le multiple sclerosis. Har'a mefuta e sa tšoaneng ea lefu lena , PPMS e nkoa e le moferefere.
Kamoo PPMS e fapaneng kateng le mefuta e meng ea MS
Sebopeho se tloaelehileng ka ho fetisisa, se tsejoang e le MS-RET (relapsing-remitting) (RRMS) , se khetholloa ka litlhaselo tse matla tse lateloang ke nako ea ho khutlisetsoa moo lefu lena le sa tsoelang pele.
Ha e tsoela pele, motho ho thoe o na le phaello ea bobeli (SPMS) .
PPMS, ka lehlakoreng le leng, e ntse e tsoela pele ho tloha qalong. Motho ea fumanoeng a e-na le PPMS ha a na li-flares kapa li khutlela morao tse amanang le RRMS kapa SPMS. Ho e-na le hoo, matšoao a hlaha butle-butle ebile ha a fetohe.
Joaloka mefuta e meng ea multiple sclerosis, tsela ea PPMS e fapane haholo, e ama motho ka mong ka tsela e fapaneng. Ba bang ba ka 'na ba ba bokooa nakong ea lilemo tse seng kae athe tse ling li lula li tsitsitse ka lilemo tse mashome.
Matšoao a amanang le Spinal Cord
Mabapi le matšoao, batho ba fumanoang ba e-na le PPMS ba atisa ho ba le mathata a ho tsamaea ka lebaka la ho atrophy (ho senya le ho senyeha) ha mokokotlo oa mokokotlo. Hape e tsejoang e le myelopathy e tsoelang pele, matšoao a ka kenyeletsa:
- Phaello e ntseng e eketseha ea marang-rang e bitsoa parasisis spastic, eo maoto a eona a tla qala ho tsitsisa, e leng se etsang hore ho bonahale eka ho na le sefahleho se bonahalang
- Bofokoli kapa ho se tsamaee ka lehlakoreng le leng la 'mele, le tsejoang e le spastic hemiparesis , e ka amang maoto, matsoho kapa matsoho
- Ho hloka mamello (ho fokotsa matla a ho ikoetlisa)
- Ho senyeha le ho hloka matla a mesifa ( ataxia )
Ha mokokotlo oa mokokotlo o angoa ke lefu lena, o ka kena-kenana le ho fetang feela ho tsamaea.
E ka baka tšenyo ea thobalano, senya le sebōpeho. Mokhathala o boetse o tloaelehile ho sena le mefuta eohle ea multiple sclerosis.
Matšoao a amanang le boko
Le hoja mokokotlo e le sepheo se ka sehloohong sa kotsi ho PPMS, boko bo ka boela ba ameha, haholo-holo karolo e tsejoang e le cerebellum e laolang ho leka-lekana le ho tsamaisana. Tsejoa e le lefu la cerebellar (PCS) le tsoelang pele, lefu lena le ama motho a le mong ho ba leshome le metso e 'meli ba fumanoang a e-na le PPMS mme a ka bonahala ka:
- Bothata ba ho tsamaea ka letsoho le letle ka lebaka la tšisinyeho e matla ea morero
- Ho lahleheloa ha molumo oa mesifa (hypotonia)
- Ho lahleheloa ke tekano (gait ataxia)
- Ho se khone ho hokahanya tsamaiso (dysmetria) moo motho a fetang overshoot kapa a sa hlokomele boemo bo entsoeng ka letsoho, leoto, kapa letsoho
- Ho se khone ho etsa mohato o potlakileng oa ho fetoha ( dysdiadochokinesia ) ho phunya ho joalo tleloubu
Ho ruruha le ho hlaphoheloa ke metsi ho bonahala e le mekhoa e ka sehloohong e etsang hore basebetsi ba PPMS ba kenye letsoho le mokokotlo oa mokokotlo.
Tse sa tloaelehang Matšoao a PPMS
Le hoja ho sa tloaelehe hakaalo, PPMS e ka ama likarolo tse ling tsa tsamaiso ea methapo e matla joaloka boko ba boko (bo pakeng tsa boko le mokokotlo oa mokokotlo) le cerebrum ('mele o moholo oa boko).
Matšoao a bonoa ho pota karolo e le 'ngoe feela ea batho ba nang le PPMS empa ba kenyeletsa:
- Mathata ka ho metsa ( dysphagia )
- Ho ba le botsoa, ho hlatsa kapa ho nyefoloha
- Ka potlako, mehato e sa itekanetseng ea mahlo ( nystagmus )
- Bothata ba pono kapa tahlehelo
- Mosebetsi oa ho utloisisa bohloko , ho akarelletsa le ho lahleheloa ke mohopolo, nako ea ho ela hloko, ho bua mantsoe, kapa ho nahana ka sebaka
Lentsoe le Tsoang ho
Ho fihlela morao tjena, ho ne ho se na lithethefatsi tse teng bakeng sa ho tšoara PPMS. Lithethefatsi tsa setso-lithethefatsi tse fetohang, joaloka Rebif le Copaxone, li sebetsa haholo ka ho fokotsa ho ruruha tse amanang le RRMS, empa li ipakile li sa sebetse ha ho phekoloa mofuta oa khatello ea kelello e bonngoeng ka PPMS.
Ka lehlohonolo, lintho li fetohile. Hona joale re na le lithethefatsi tse tsejoang e le Ocrevus (ocrelizumab) e khonang ho tšoara PPMS hammoho le ho khutlisa mefuta ea lefu lena. E amoheleha ke US Food and Drug Administration (FDA) ka March 2017, Ocrevus e nkoa e le e kholo ea papali ea papali 'me e tla ntlafatsa bophelo ba ba phelang le mofuta ona o sa tloaelehang oa multiple sclerosis.
> Mohloli
> Ohrbach, R .; Zhao, A .; Wang, Y. le al. "Ho bapisoa le Maloetse Mosebetsing oa SPMS le PPMS ho latela Molao oa Multicenter Clinical Trials." PLoS One 2012; DOI 10.1371 / journal.pone.0045409.
> Tsamaiso ea Tsamaiso ea Lijo le Meriana ea US. "Injection ea Ocrevus (ocrelizumab)." Silver Spring, Maryland; La 28 March, 2017.