Khetho ea Maloetse: Mofuta o sa Tšoaneng oa Phatlalatso ea Frontotemporal Dementia

Mofuta ona oa ho tsoaloa ha Frontotemporal o boetse o tsejoa e le Mathata a Pick

Mofuta o fapaneng oa boitšoaro oa frontotemporal dementia (bvFTD) ke o mong oa mefuta e 'maloa ea dementias e oelang "sethatsong sa" frontotemporal ". Sehlopha sena se ama batho ba ka bang 50 000 ho isa ho 60,000 Maamerika. Joalokaha lebitso le bontša, mofuta ona oa 'dementia' o ama haholo-holo li-lobes tsa pele le tsa nako ea boko. Bothata bo tloaelehileng ka ho fetisisa ba frontotemporal ke ba mofuta o mong oa boitšoaro.

Ho ba le maikutlo a mangata a ho fetola maikutlo a pele-'momoropong ka linako tse ling ho thoe ke lefu la Pick .

Ke Eng e Bakang Mafu a Pick?

Ho nahanoa hore lefu la Pick le bakoa ke ho hlophisa ka tsela e sa tloaelehang ea liprotheine tsa tau ka lobes ea pele le ea nako ea boko. Likokoana-hloko tsena tsa protheine li tsejoa e le 'mele ea ho khetha. Ha li ntse li bokella li-lobes tsena, lisele tsa boko li qala ho shoa, li baka liphetoho tsa maikutlo, tsa boitšoaro le tsa tsebo mosebetsing oa hau.

Matšoao

Matšoao a tloaelehileng ka ho fetisisa a bvFTD ke mathata a boitšoaro kapa a maikutlo , ho kenyeletsa ho ja haholo, ho ba le maikutlo a sa lokelang, ho etsa likarabo tse sa lokelang, le ho bontša moqoqo le liketso tse amanang le maikutlo , hammoho le ho halefa, ho ferekana , ho hloka thahasello le boithati.

Batho ba nang le bvFTD ba ka 'na ba thatafalloa ho boloka mosebetsi, ba bontša ho fokotseha ha bohloeki ba bona, ba boloka lintho tse itseng, ba etsa liqeto tse fokolang tsa lichelete, litho tsa malapa le metsoalle ka lebaka la maikutlo a bona a sa tsotelleng le boitšoaro.

Batho ba bang ba nang le bvFTD ba boetse ba bona mathata a tsamaiso a tšoanang le lefu la Parkinson , ho kenyelletsa le ho fokotsa sefahleho sa sefahleho, boima ba mesifa, bofokoli le botsitso.

Ho fapana le Alzheimer's , ho lahleheloa kelellong hangata ha ho hlahe ka bvFTD, 'me haeba ho joalo, ha ho fihlela lefu lena e le mekhahlelo ea eona hamorao.

Joaloka mohlokomeli, u ka 'na ua hlokomela mathata a ho hopola, hammoho le liphephetso ka ho hlophisa kapa ho ela hloko (ho amana le tshebetso ea tsamaiso ).

Ka bvFTD e matla, puo e boetse e ameha, ho etsa hore puisano e be thata haholo.

Matšoao a Pick a fapane joang le a Alzheimer's?

Mofuta o fapaneng oa boitšoaro oa foreotemporal dementia (lefu la Pick) o na le matšoao a mangata a fetang a lefu la Alzheimer ho tloha ha mafu a mabeli a atisa ho ama kutloisiso, maikutlo le boitšoaro. Leha ho le joalo, matšoao a pepenene a lefu la Pick, haholo-holo, a na le liphetoho moeeng, kahlolo , tsamaiso ea boits'oaro le boitšoaro, ha ka lefu la Alzheimer, ho hopola mohopolo, mokhoa oa ho bua le ho fokotsa puisano ho tloaelehile qalong.

Tsejoa

Ho lemoha ha BvFTD ho atisa ho lieha hobane qalong ho ka 'na ha nahanoa hore motho ea amehileng o mpa a le bobebe, boithati, a tepeletse maikutlo kapa a itšoara ka setso. Ha matšoao a ntse a tsoela pele, leha ho le joalo malapa a atisa ho batla thuso ea ngaka bakeng sa ho hlahlojoa le kalafo. Ho lemoha ho itšetlehile ka boteng ba matšoao a mangata a boletsoeng ka holimo, hammoho le matla a ho laola 'dementia' e 'ngoe e kang Alzheimer's kapa ' dementia 'ea masapo . Ho hlahloba litekanyetso tsa molao bakeng sa FTD e fapaneng ea boitšoaro ho ka ba molemo ho litho tsa lelapa haeba BvFTD e fumanoa kapa e nkoa ke ngaka.

MRI e ka boela ea thusa ho hlahloba bvFTD hobane hangata e tla bontša ho hlahisa li -atrophy (shrinkage) tsa lobe ea pele ea boko. Ha lefu lena le ntse le tsoela pele, ho fokotseha ho tla eketseha le ho hasana libakeng tsa nakoana, hammoho le basal ganglia.

Ho itšireletsa le ho lebella Bophelo (Pono ea nako e telele)

Karolelano ea tebello ea bophelo ho tloha qalong ea matšoao ke lilemo tse ka bang tse robeli ho isa ho tse robong, le hoja batho ba bang ba ka phela lilemo tse 20 kapa ho joalo ka lefu lena. Joaloka tabeng ea 'dementia' efe ​​kapa efe, e ka ba lefu le boima bakeng sa bahlokomeli, hammoho le ba nang le lona.

Phekolo

Kalafo e ka 'na ea e-ba le ho leka ho sebelisa mekhoa e seng mekhoa ea boitšoaro ho thibela boitšoaro bo itseng.

Lingaka tse ling li fana ka li-anti-depressing tse bitsoang serotonin reuptake inhibitors (SSRIs) tse khethollang, tse ka 'nang tsa thusa ka tse ling tsa boitšoaro bo qobelloang bo kang ho lata kapa ho ja lijo tse ngata.

Lentsoe ho

Ho tloaelehile hore u ikutloe u sithabetse ka linako tse ling ha u sebetsana le mathata a boitšoaro bo fapaneng le a foreotemporal dementia. Hlokomoloha teko ea ho leka ho e etsa kaofela; ho e-na le hoo, batla thuso ho ba u potolohileng, ebang ke ka lenane la tšehetso ea sechaba, puisano ea Inthanete ka BvFTD kapa motsoalle ea ikemiselitseng ho u ntša kofi kapa a lule hae le moratuoa oa hau ha u ntse u robala.

Ho phaella moo, Mokhatlo oa Frontotemporal Dementia o thathamisa lihlopha tsa tšehetso sebakeng sa heno hammoho le lisebelisoa tsa inthanete le mohala oa fono bakeng sa thuso.

Lisebelisoa:

Annals ea Neurology. Ho ja le hypothalamus liphetoho tsa boitšoaro-tse fapaneng le bothata ba 'dementia' ea frontotemporal. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3084499

Mokhatlo oa Kopano ea Frontotemporal. Litekanyetso tsa machaba tsa tumellano bakeng sa mekhoa e fapaneng ea boitšoaro ea FTD. http://www.theaftd.org/wp-content/uploads/2009/02/Table-3-International-consensus-criteria-for-behavioural-variant-FTD.pdf

Banks, S., Weintraub, S. Journal ea Geriatric Psychiatry le Neurology. Matšoao a Neuropsychiatric Tseleng e Tšoanang ea Boitšoaro Frontotemporal Dementia le Akhasia e Khōlō ea Pele .. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2892801/

Neurology. Ho hlokomeleha ha maemo a hona joale bakeng sa ho hlahlojoa ha boitšoaro bo fapaneng ho fapana le bothata ba 'dementia' ea frontotemporal. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2821829/

Univesithi ea California, San Francisco. Tsoelo-pele ea mafu: Tsela e fapaneng ea boitšoaro FTD. http://memory.ucsf.edu/ftd/overview/ftd/progression/multiple