Lisele tsa 'mele ka hare ke likaroloana tse nyane tse bitsoang mitochondria (tse ka bang 1 000 ka sele). Mitochondria e hlahisa matla lisele tsa rona li hloka ho hōla le ho sebetsa. Haeba mitochondria e senyehile kapa e sa sebetse, lisele li sitoa ho phetha mesebetsi ea tsona 'me li ka tsoa likotsi kapa tsa shoa. Lisele tsena tse lemetseng kapa tse sa sebetseng li qetella li baka lefu la mitochondrial.
Lefu la mitochondrial le ka ba thata ho fumana lefu hobane lefu lena le ka hlahisa matšoao a fapa-fapaneng, ho tloha bofokoling ho ea boemong bo matla. Ho na le mefuta e mengata ea mefuta e fapaneng ea mafu a mitochondrial. Mofuta oo u itšetlehileng ka oona ke hore na ke lisele life tse amehang. Mathata a ka 'na a qala ha a hlaha kapa a hlaha hamorao. Boholo ba linyeoe li fumanoa nakong ea bongoaneng, le hoja linyeoe tsa batho ba baholo li qala ho feta. Lefu la mitochondrial le ama ba pakeng tsa 40,000 le 70,000 ba Amerika, ba hlahang ho e mong ho bana ba 2 500 ho isa ho 4 000.
Lefu la mitochondrial ke lefutso . Lefu lena le ka ba lefa ho batsoali ba lona kapa ka lebaka la phetoho e sa fetoheng DNA ea hau. Mitochondria e ka boela ea lematsoa ho sebelisoa ke lithethefatsi kapa tsenyo e bakoang ke li-radicals tsa mahala (limolek'hule tse senyang). Palo e kholo ea liphetoho tsa lefutso e ka baka lefu lena. Leha ho le joalo, phetoho e tšoanang ho batho ba babeli ba fapaneng e ka 'na ea se ke ea hlahisa matšoao a tšoanang.
Matšoao le Matšoao
Kaha mitochondria e teng karolong ea 90 lekholong ea lisele tsa rōna, litho tse fapa-fapaneng li ka ameha ho akarelletsa le boko le mesifa. Mesebetsi e amehang ka ho fetisisa ke boko, pelo, sebete, mesifa ea masapo, liphio, le endocrine le mekhoa ea ho hema. Matšoao ao u nang le 'ona a itšetlehile ka hore na lisele le likarolo li ameha joang, li ka kenyelletsa:
- Boko: ho lieha ho ntlafatsa, ho lieha kelellong, ho tsieleha , ho tepella maikutlo
- Metsing: bofokoli, bohloko
- Matsoho: bofokoli, molumo o tlaase, ho senya, bohloko
- Boloetse ba pelo
- Mahlo: ho senya , ho lahleheloa ke pono
- Maloetse a liphio
- Mathata a ho hema
- Tahlehelo ea kutlo
Matšoao a mang a kenyeletsa mathata a bakoang ke masapo , bothata ba ho koenya, lefu la pelo, lefu la sebete, lefu la tsoekere , lactic acidosis le monyetla o eketsehileng oa ho fumana tšoaetso. Ho bana, lefu lena le ka boela la etsa hore ho be le ho lieha ho hola le tsoelo-pele ea tsoelo-pele. Ho lemoha lefu la mitochondrial hangata ho boima hobane matšoao a sa tšoane 'me a ka etsisa maemo a mang. Ts'ebetso e mengata ea tsamaiso ea likarolo, likarolo tse tharo kapa ho feta, hangata e bontša lefu la mitochondrial.
Phekolo
Matšoao a mangata a lefu la mitochondrial a ka fumanoa ka ho hlaseloa ke mesifa. Makhotho a mang a ho hlahloba a kenyeletsa liteko tsa mali , tlhahlobo ea liphatsa tsa lefutso le tlhahlobo ea enzyme. Li-biopsies tsa mesifa le liteko tse ling li ka theko e boima haholo, li tlohela linyeoe hore li fumanoe tseleng ea kliniki feela.
Ha ho na pheko ea lefu la mitochondrial. Li-supplement-thiamine ( B1 ), riboflavin (B12), vithamine C , vithamine E, lipoic acid le coenzyme Q10 - li ka thusa ho tšoara likarolo tse itseng tsa lefu lena. Ho qoba khatello ea maikutlo ho ka boela ha thusa ho fokotsa matšoao
Hona joale bafuputsi ba sheba lithethefatsi tse ka thibelang lactic acid buildup e amanang le lefu la mitochondrial. Ba bang ba leka lijo tse tlaase haholo tsa lik'habohaedreite ho fokotsa mosebetsi oa mitochondria.
Ho kopanya ho se sebetse ha Mitochondrial ho Mafu a mang
Bafuputsi ba ithuta lefu la mitochondrial bakeng sa lintlha tse ling tse kang kankere, lefu la Parkinson, maloetse a Alzheimer le mafu a pelo. Tšenyo ea mitochondria e nahanoa hore e amahanngoa le maemo ao kaofela. Ho senya ha mitochondrial bophelo bohle bo ka ba karolo ea botsofali.
> Mehloli:
> Foreman, J. Mafu a ka ama matla a lisele tsa rona. The Boston Globe , la 17 June, 2003.
> Mokhatlo oa Machachondrial Disease Foundation.